Esta buscando: Methyl-2-hydroxyisobutyrate


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Numero del catalogo: (ACRO436180050)
Proveedor: Thermo Scientific
Descripción: Methyl (R)-(-)-3-hydroxyisobutyrate 98%
UOM: 1 * 5 g

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Proveedor: Apollo Scientific
Descripción: Methyl-2-hydroxyisobutyrate 95%

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Proveedor: TCI
Descripción: Methyl (R)-(-)-3-hydroxyisobutyrate ≥99.0% (por GC)

Proveedor: Apollo Scientific
Descripción: Methyl (R)-(-)-3-hydroxyisobutyrate 97%

Proveedor: TCI
Descripción: Methyl-2-hydroxyisobutyrate ≥99.5% (por GC)

Proveedor: Thermo Scientific
Descripción: Appearance: Clear colorless Liquid
Proveedor: Thermo Scientific
Descripción: (S)-(+)-Methyl-3-hydroxy-2-methylpropionate ≥98%
Proveedor: Thermo Scientific
Descripción: 2-Hidroxi-2-metilpropionato de etilo ≥98%
Proveedor: TCI
Descripción: 2-Hidroxi-2-metilpropionato de etilo ≥98.0% (por GC)

Numero del catalogo: (BOSSBS-15483R-HRP)
Proveedor: Bioss
Descripción: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.
UOM: 1 * 100 µl


Numero del catalogo: (BOSSBS-15483R)
Proveedor: Bioss
Descripción: HIBADH is a 336 amino acid mitochondrial enzyme that catalyzes the NAD+-dependent, reversible oxidization of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7.0 and 10.0, with optimal activity between 8.8 and 9.0. It was previously hypothesized that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterized by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.
UOM: 1 * 100 µl


Numero del catalogo: (BOSSBS-15483R-CY7)
Proveedor: Bioss
Descripción: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.
UOM: 1 * 100 µl


Numero del catalogo: (BOSSBS-15483R-A647)
Proveedor: Bioss
Descripción: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.
UOM: 1 * 100 µl


Proveedor: Thermo Scientific
Descripción: Ácido 2-hidroxiisobutírico 98%
Proveedor: Apollo Scientific
Descripción: (R)-3,3,3-Trifluoro-2-hydroxy-2-methylpropionic acid 97%

Proveedor: Apollo Scientific
Descripción: (S)-3,3,3-Trifluoro-2-hydroxy-2-methylpropionic acid 95+%

Consulta de precio
El stock para este material es limitada pero puede estar disponible en un almacén cerca de usted. Por favor, asegúrese de que ha iniciado sesión en la web para que el stock disponible se puede mostrar. Si el call sigue apareciendo y usted necesita ayuda, por favor llámenos al 902 222 897 o por email en webshop.es@avantorsciences.com.
El stock para este material es limitada pero puede estar disponible en un almacén cerca de usted. Por favor, asegúrese de que ha iniciado sesión en la web para que el stock disponible se puede mostrar. Si el call sigue apareciendo y usted necesita ayuda, por favor llámenos al 902 222 897 o por email en webshop.es@avantorsciences.com.
Este producto se trata de un artículo regulado sometido a normativa que restringe su venta. Si procede, nos pondremos en contacto con usted para solicitarle la licencia o declaración de uso necesaria para poder proceder al suministro del producto.
Este producto se trata de un artículo regulado sometido a normativa que restringe su venta.
Si procede, nos pondremos en contacto con usted para solicitarle la licencia o declaración de uso necesaria para poder proceder al suministro del producto.
Este producto ha sido bloqueado por su organización. Por favor, pónganse en contacto con su departamento de compras para obtener más información.
El producto original ya no está disponible. Su sustituto se muestra a continuación.
El producto(s) marcados con este símbolo están descatalogados - se venden hasta acabar stock. Pueden encontrar alternativas buscando con el número de catálogo VWR listado arriba. Si necesita más ayuda, por favor llame al Servicio de atención al cliente de VWR al 902.222.897.
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